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Die Toxine verbleiben im Blut und verteilen sich so im gesamten Körper, was schlussendlich zu Symptomen führt. \nEin entwickelter portosystemischer Shunt resultiert zumeist aus vorangehenden Lebererkrankungen, welche verursachen, dass eine Akkumulation von Toxinen entsteht. Die Symptome variieren, erscheinen jedoch in der Regel immer nach der Futteraufnahme. Häufige Symptome sind Erbrechen, Durchfall, vermehrter Durst und Urinabsatz, Lethargie, Verwirrtheit und Orientierungslosigkeit. \nDie angeborene Form tritt deutlich häufiger auf und wird somit meistens im Welpenalter diagnostiziert. \nDie Diagnostik setzt sich aus Blut- und Urin- sowie einer Ultraschalluntersuchung zusammen. \nIn den häufigeren Fällen bedarf es einer Operation zur Behebung des Problems, manchmal ist jedoch auch eine rein medikamentöse Behandlung möglich. 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